Which type of immunodeficiency disorder is inherited in an X-linked recessive pattern and primarily affects males, leading to the absence of mature B cells and immunoglobulins?
Selective IgA deficiency
DiGeorge syndrome
X-linked agammaglobulinemia
Severe combined immunodeficiency (SCID)
The Correct Answer is C
Explanation: The correct answer is c. X-linked agammaglobulinemia. This disorder primarily affects males and is caused by mutations in the BTK gene, resulting in a lack of mature B cells and immunoglobulins.
Incorrect choices:
a. Selective IgA deficiency is a primary immunodeficiency disorder characterized by a deficiency of immunoglobulin A (IgA), and it can affect both males and females.
b. DiGeorge syndrome is caused by a chromosome 22 deletion and is not inherited in an X-linked recessive pattern.
d. Severe combined immunodeficiency (SCID) is a group of disorders that can be inherited in various patterns, including autosomal recessive, autosomal dominant, or X-linked recessive. SCID affects both males and females and results in a severe deficiency of T cells, B cells, and natural killer (NK) cells.
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Naxlex Comprehensive Predictor Exams
Related Questions
Correct Answer is D
Explanation
Explanation: The correct answer is d. Educating the client on proper hand hygiene. Educating the client on proper hand hygiene is essential to reduce the risk of infections in individuals with immunodeficiency disorders. Frequent handwashing is a simple yet effective way to prevent the transmission of infectious agents.
Incorrect choices:
a. Administering live vaccines is contraindicated for clients with immunodeficiency disorders, as live vaccines contain weakened pathogens that can cause serious infections in this population.
b. Encouraging the client to perform strenuous physical activities is not appropriate for someone with immunodeficiency, as strenuous activities can put additional strain on the immune system and increase the risk of infections.
c. Limiting the client's intake of fluids is not a necessary intervention for immunodeficiency disorders. Adequate fluid intake is generally important for overall health, but it is not directly related to managing immunodeficiency disorders.
Correct Answer is C
Explanation
The correct answer is c. Ataxia-telangiectasia. Ataxia-telangiectasia is a rare genetic disorder that affects the cerebellum, causing poor muscle coordination (ataxia) and small, dilated blood vessels (telangiectasias). It also leads to defective T-cell function, making affected individuals more susceptible to infections.
Incorrect choices:
a. X-linked agammaglobulinemia (XLA) is a primary immunodeficiency disorder that primarily affects B-cell function, leading to a lack of mature B cells and low levels of immunoglobulins, but does not involve defective T-cell function.
b. Selective immunoglobulin A (IgA) deficiency is characterized by a deficiency of IgA, but it does not typically lead to defective T-cell function.
d. DiGeorge syndrome is caused by a deletion on chromosome 22 and primarily affects the development of certain organs, including the thymus and parathyroid glands, resulting in T-cell deficiency. While it may lead to some B-cell abnormalities, defective T-cell function is the hallmark of this disorder.
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